CDB25:0003857 LAMB1 — DAG1

Experimentally validated in Mixed species; Orthology-inferred in Human, Mouse, Rat, Frog, Zebrafish, Chicken, Macaque, Pig, Dog, Cow, Chimp, Horse, Marmoset, Sheep

Title

Journal:; Year Published:

Abstract

Brain alpha-dystroglycan displays unique glycoepitopes and preferential binding to laminin-10/11.

FEBS letters, 2006; PubMed, Mus Musculus Lamb1 — Bos taurus DAG1
ABSTRACT: alpha-Dystroglycan was quantitatively enriched from mammalian brain based on its uniform reactivity with Vicia villosa agglutinin and resolved into sub-populations possessing or lacking the sulfated glucuronic acid epitope recognized by monoclonal antibody HNK-1. We generated a new monoclonal antibody specific for a glycoepitope on brain alpha-dystroglycan but absent from alpha-dystroglycan expressed in all other tissues examined. Finally, we found that laminin-10/11 preferentially bound to brain alpha-dystroglycan compared to skeletal muscle alpha-dystroglycan. Our results suggest that tissue-specific glycosylation modifies the laminin binding specificity of alpha-dystroglycan.

Dystroglycan is a binding protein of laminin and merosin in peripheral nerve.

FEBS letters, 1994; PubMed, Mus Musculus Lamb1 — Oryctolagus cuniculus DAG1
ABSTRACT: alpha-Dystroglycan, a 156 kDa dystrophin-associated glycoprotein, binds laminin in skeletal muscle. Here we demonstrate that alpha-dystroglycan is a binding protein of laminin (A/B1/B2) and merosin (M/B1/B2) in peripheral nerve. Immunocytochemical analysis demonstrates the localization of alpha-dystroglycan and merosin surrounding myelin sheath of peripheral nerve fibers. Biochemical analysis demonstrates that the 120 kDa peripheral nerve alpha-dystroglycan binds merosin as well as laminin. The binding of laminin and merosin is Ca2+ dependent and is inhibited by NaCl and heparin. Recently, merosin was shown to be deficient in the peripheral nerve of dy mice which have defects in myelination. The interaction between alpha-dystroglycan and merosin may play a role in the regulation of Schwann cell myelination and/or maintenance of myelin sheath.
Basic Information on LAMB1
Ligand Name: laminin subunit beta 1
Other Symbols: CLM
Ligand Location: secreted based on perplexity, uniprot
HGNC Gene Symbol Report: LAMB1
GeneCards: LAMB1
HGNC Gene Group: Laminin subunits
Interactions with other Receptors for LAMB1
Basic Information on DAG1
Receptor Name: dystroglycan 1
Other Symbols: A3a, 156DAG, AGRNR, DAG
Receptor Location: cell membrane based on hpa, perplexity, uniprot
HGNC Gene Symbol Report: DAG1
GeneCards: DAG1
HGNC Gene Group: unknown